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Human Gene Knockin

Humanized Mouse Models

Since 1998, ingenious targeting laboratory has generated hundreds of humanized mouse models for researchers and pharmaceutical companies worldwide. Our humanized models have supported therapeutic development programs across immuno-oncology, metabolic disease, neuroscience, and other areas, with results published in peer reviewed journals.

Humanized mouse models express human proteins or protein domains in place of their mouse counterparts. This humanization enables testing of human specific therapeutics, study of human specific biology, and improved translation from preclinical models to clinical outcomes.

100s
Humanized Models
800+
Publications
26+
Years Experience
100%
Success Rate

Why Humanize Mouse Genes

Species Specific Therapeutics

Many therapeutic antibodies and biologics are designed specifically for human targets:

  • Therapeutic antibodies may not cross react with mouse orthologs
  • Human specific epitopes require human sequence for binding
  • Biologics may have species specific receptor interactions
  • Humanized models enable efficacy testing of clinical candidates

Translational Relevance

Humanized models improve translation to clinical outcomes:

  • Study human specific protein functions
  • Model human specific disease mechanisms
  • Evaluate pharmacokinetics with human target engagement
  • Develop and validate human specific biomarkers

Regulatory Considerations

Humanized models support regulatory submissions:

  • Demonstrate on target efficacy with human target
  • Evaluate safety in context of human target biology
  • Support mechanism of action characterization
  • Enable pharmacodynamic biomarker development

Humanization Strategies

Complete Gene Replacement

The entire mouse gene is replaced with the human ortholog:

  • Human coding sequence under mouse regulatory control
  • Preserves mouse expression pattern and level
  • Enables study of all human specific protein features
  • Most comprehensive humanization approach

Complete replacement is appropriate when the entire protein sequence differs functionally between species or when studying human specific splice variants.

Extracellular Domain Humanization

Human extracellular domain replaces mouse sequence while retaining mouse intracellular domain:

  • Human epitopes for antibody binding
  • Mouse signaling domains for normal downstream function
  • Commonly used for immune checkpoint humanization
  • Maintains compatibility with mouse immune system

This approach is ideal for therapeutic antibody testing where the antibody targets extracellular epitopes.

Specific Domain or Epitope Humanization

Only the specific region recognized by the therapeutic is humanized:

  • Minimal sequence change
  • Preserves most mouse protein function
  • Targeted to specific antibody epitope
  • May require epitope mapping data

Humanized Regulatory Elements

Human promoter or enhancer sequences replace mouse regulatory regions:

  • Study human specific gene regulation
  • Model human expression patterns
  • Investigate human specific enhancer variants
Proprietary Technology

TruHumanization™ Technology

ingenious targeting laboratory's proprietary TruHumanization™ technology optimizes humanization strategies for maximum therapeutic relevance and physiological compatibility with complete gene replacement.

Quality Assurance: All TruHumanization™ projects include pre-germline analysis to verify correct human sequence integration before mouse generation.

Applications by Therapeutic Area

Immuno Oncology

Humanized immune checkpoint models are essential for cancer immunotherapy development:

Dual humanized models (e.g., PD1 + CTLA4) enable combination immunotherapy evaluation.

Learn more

Metabolic Disease

Humanized metabolic targets support therapeutic development:

  • Humanized receptors for peptide therapeutic testing (GLP1R, GCGR)
  • Humanized enzymes for small molecule drug development
  • Humanized lipoproteins for cardiovascular studies
  • Humanized transporters for pharmacokinetic evaluation
Learn more

Neuroscience

Humanized CNS targets enable neurotherapeutic development:

  • Humanized amyloid precursor protein (APP) for Alzheimer studies
  • Humanized tau (MAPT) for tauopathy research
  • Humanized receptors for antibody or biologic testing
  • Humanized ion channels for species specific pharmacology
Learn more

Infectious Disease

Humanized receptors enable infection and therapeutic studies:

  • Humanized viral entry receptors
  • Humanized immune components for vaccine studies
  • Humanized targets for antiviral therapeutic testing

Strain Background

Choose strain background based on experimental requirements:

C57BL/6

Most common, compatible with syngeneic tumor models (MC38, B16)

BALB/c

Alternative background, compatible with CT26, 4T1 tumors

Immunodeficient backgrounds

For human immune cell engraftment studies

Learn more about strain backgrounds

Combining Multiple Humanizations

Complex models may require multiple humanized genes:

  • Dual checkpoint humanization (PD1 + CTLA4, PD1 + LAG3)
  • Receptor ligand pairs (CD47 + SIRPα)
  • Pathway components (multiple targets in same pathway)

Breeding strategies or sequential targeting can combine multiple humanized alleles.

Humanized Checkpoint Models

TargetHumanization ApproachApplications
PD1 (PDCD1)Extracellular domainAnti PD1 antibody efficacy
PDL1 (CD274)Extracellular domainAnti PDL1 antibody efficacy
CTLA4Extracellular domainAnti CTLA4 antibody efficacy
LAG3Extracellular domainLAG3 inhibitor evaluation
TIM3Extracellular domainTIM3 pathway studies
TIGITExtracellular domainTIGIT inhibitor development
CD47Extracellular domainAnti CD47 antibody efficacy
SIRPαExtracellular domainCD47 SIRPα axis studies

What Researchers Say

We are very happy with this mouse line and we're not done yet. There's still plenty to do. The versatility of the F.A.S.T.™ approach is really unparalleled. There are so many possibilities to use the cassette that one paper does not showcase it all. Also, the addition of N-terminal GFP has helped quite a bit to understand gene expression patterns.

Frank Bosmans, PhD

Ghent University, Belgium

View All Testimonials

Start Your Humanization Project

Our scientific consultants are ready to discuss your humanization requirements and recommend the optimal strategy for your therapeutic program. Initial consultation is provided at no charge and includes humanization approach recommendations, allele design options, and timeline estimates.

Key Terms

Understanding the terminology used in humanized mouse model generation helps you communicate effectively with our scientific team and interpret project documentation.

Humanized Mouse

A mouse model where a mouse gene or genomic region has been replaced with the corresponding human sequence, enabling study of human-specific biology.

Gene Replacement

A targeting strategy that substitutes mouse genomic sequences with human equivalents to model human-specific biology or test human-targeted therapies.

BAC (Bacterial Artificial Chromosome)

A DNA construct used for cloning large DNA fragments (100-300 kb) in bacteria, used for large-scale humanization projects.

Chimera

An organism composed of cells derived from two or more different sources, used to establish germline transmission of targeted alleles.

View Complete Glossary
✦ New for 2026

Breeding Scheme Architect

Plan complex multi-allele breeding strategies, calculate expected genotype ratios, and estimate time to experimental cohorts—all before starting your project.

Visualize multi-generation breeding paths
Calculate Mendelian ratios automatically
Estimate timeline to study ready cohorts

Free Research Tool

No account required

Allele 1Gene-flox (conditional)
Allele 2Cre-driver (tissue-specific)
TargetHomozygous knockout

→ 3 generations to target genotype

Lab Signals

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Frequently Asked Questions

Many therapeutic antibodies and biologics are designed to target human proteins and do not cross-react with mouse orthologs. Humanized mice express human target proteins, enabling efficacy testing of human-specific therapeutics in an immunocompetent mouse with a functional immune system.

Full gene replacement substitutes the entire mouse gene with human sequence, including regulatory elements. Extracellular domain humanization replaces only the portion of the protein that therapeutic antibodies recognize, while preserving mouse intracellular domains for proper signaling. ECD humanization is often sufficient for antibody testing and may be faster to generate using knockin strategies.

Yes. Dual or triple humanized mice are commonly used for combination therapy studies. For example, PD1/CTLA4 double humanized mice enable testing of dual checkpoint blockade. Multiple humanizations can be combined through breeding or sequential targeting.

ingenious targeting laboratory offers humanized immune checkpoint models for PD1, PDL1, CTLA4, LAG3, and TIM3, and others, as well as combinations. These models express human checkpoint proteins recognized by clinical antibodies while maintaining functional mouse immune systems for syngeneic tumor studies.

Looking for detailed technical information?

View our comprehensive legacy documentation with in-depth specifications.

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